Steven R. Cohen

All articles by Steven R. Cohen

Buschke-Ollendorff syndrome (dermatofibrosis lenticularis disseminata, connective tissue nevus with osteopoikilosis)

Are You Confident of the Diagnosis? Buschke-Ollendorff syndrome (BOS) describes an autosomal dominant condition that encompasses connective tissue nevi and osteopoikilosis. The skin findings of BOS are primarily skin-colored to yellow papules, which may coalesce into plaques. As these cutaneous findings are not unique to the syndrome, both osteopoikilosis and a positive family history are…

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